產(chǎn)品編號(hào) | bsm-62867R |
英文名稱 | SDHC Recombinant Rabbit mAb |
中文名稱 | 琥珀酸細(xì)胞色素亞基B560重組兔單抗 |
別 名 | CYBL; PGL3; QPs1; SDH3; sdhC. |
抗體來源 | Rabbit |
克隆類型 | Recombinant |
交叉反應(yīng) | Human,Mouse,Rat |
產(chǎn)品應(yīng)用 | WB=1:500-2000,IHC-P=1:50-200,IHC-F=1:50-200,IF=1:50-200
not yet tested in other applications. optimal dilutions/concentrations should be determined by the end user. |
理論分子量 | 19 kDa |
檢測(cè)分子量 | 17 |
性 狀 | Liquid |
免 疫 原 | KLH conjugated synthetic peptide derived from human SDHC |
亞 型 | IgG |
純化方法 | affinity purified by Protein A |
緩 沖 液 | 10mM phosphate buffered saline(pH 7.4) with 150mM sodium chloride, 0.05% BSA, 0.02% sodium azide and 50% glycerol. |
保存條件 | Store at 4℃ for short term. Store at -20℃ for long term. Avoid repeated freeze/thaw cycles. |
注意事項(xiàng) | This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications. |
PubMed | PubMed |
產(chǎn)品介紹 |
Membrane-anchoring subunit of succinate dehydrogenase (SDH) that is involved in complex II of the mitochondrial electron transport chain and is responsible for transferring electrons from succinate to ubiquinone. SWISS: Q99643 Gene ID: 6391 Involvement in disease:Defects in SDHC are the cause of hereditary paragangliomas type 3 (PGL3) [MIM:605373]; also known as autosomal dominant non-chromaffin paragangliomas type 3. Non-chromaffin paragangliomas are usually benign, neural crest derived tum |
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