强伦轩一级A片在线观看,中文字幕乱码人妻二区三区,鲁鲁狠狠狠7777一区二区,西西4444www无码精品
掃碼關(guān)注公眾號(hào)           掃碼咨詢技術(shù)支持           掃碼咨詢技術(shù)服務(wù)
  
客服熱線:400-901-9800  客服QQ:4009019800  技術(shù)答疑  技術(shù)支持  質(zhì)量反饋  關(guān)于我們  聯(lián)系我們
黄色视频网站在线观看,丰满放荡岳乱妇91wW,寡妇熟妇高潮片AAA
Rabbit Anti-ACADS/BF488 Conjugated antibody (bs-23057R-BF488)
訂購熱線:400-901-9800
訂購郵箱:sales@bioss.com.cn
訂購QQ:  400-901-9800
技術(shù)支持:techsupport@bioss.com.cn
說 明 書: 100ul  
100ul/2980.00元
大包裝/詢價(jià)
產(chǎn)品編號(hào) bs-23057R-BF488
英文名稱 Rabbit Anti-ACADS/BF488 Conjugated antibody
中文名稱 BF488標(biāo)記的酰基輔酶A脫氫酶短鏈抗體
別    名 ACAD3; Acyl Coenzyme A dehydrogenase, C2 to C3 short chain; Acyl-CoA dehydrogenase, C2 to C3 short chain; Acyl-CoA dehydrogenase, short chain; Acyl-Coenzyme A dehydrogenase, short chain; AI196007; Bcd-1; Bcd1; Butyryl CoA dehydrogenase; EC 1.3.99.2; SCAD; Short chain acyl CoA dehydrogenase; Short-chain specific acyl-CoA dehydrogenase, mitochondrial; Unsaturated acyl CoA reductase; ACADS_HUMAN.  
規(guī)格價(jià)格 100ul/2980元 購買        大包裝/詢價(jià)
說 明 書 100ul  
研究領(lǐng)域 腫瘤  細(xì)胞生物  免疫學(xué)  轉(zhuǎn)錄調(diào)節(jié)因子  線粒體  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應(yīng) (predicted: Human, Mouse, Rat, Pig, Cow, )
產(chǎn)品應(yīng)用 ICC=1:50-200 IF=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 45kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human ACADS
亞    型 IgG
純化方法 affinity purified by Protein A
儲(chǔ) 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產(chǎn)品介紹 background:
ACADS is a homotetramer mitochondrial flavoprotein, which is a member of the acyl CoA dehydrogenase family. This enzyme catalyzes the initial step of the mitochondrial fatty acid beta oxidation pathway. Mutations in this gene have been associated with Short Chain Acyl CoA Dehydrogenase Deficiency.

Subcellular Location:
Mitochondrion matrix.

DISEASE:
Defects in ACADS are the cause of acyl-CoA dehydrogenase short-chain deficiency (ACADSD) [MIM:201470]. It is an autosomal recessive disorder resulting in acute acidosis and muscle weakness in infants, and a form of lipid-storage myopathy in adults.

Similarity:
Belongs to the acyl-CoA dehydrogenase family.

Database links:

Entrez Gene: 35 Human

Entrez Gene: 11409 Mouse

Entrez Gene: 64304 Rat

Omim: 606885 Human

SwissProt: P16219 Human

SwissProt: Q07417 Mouse

SwissProt: P15651 Rat

Unigene: 507076 Human

Unigene: 18759 Mouse

Unigene: 1167 Rat



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權(quán)所有 2004-2026 www.nmgps.com 北京博奧森生物技術(shù)有限公司
通過國際質(zhì)量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號(hào): 00124Q34771R2M/1100
通過國際醫(yī)療器械-質(zhì)量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號(hào): CQC24QY10047R0M/1100
京ICP備05066980號(hào)-1         京公網(wǎng)安備110107000727號(hào)
人妻夜夜女同中文字幕 | 欧美精品videosex极品 | 欧美国产日韩一区二区 | 无码人妻aⅴ一区二区三区有奶水 | 免费黄网站久久久 | 国产露脸农村妇女对白 | 在线免费观看美女AV | 亚洲一区二区影院 | 妺妺窝人体色444444大粗 | 精品国产一级A片黄毛网站 国产精品偷乱一区二区三区 | 黄视频在线免费看 | 欧美黄网站在线免费播放 | 免费一级婬片AA片观看 | 色情午夜 码一区二区 | 国产免费小视频在线观看 | 日本中文字幕理论片 | 波多野吉衣无码内射精品视频 | 永久免费看mv网站入口亚洲 | 波多野结衣av一区二区蜜桃观看 | 黄色操逼小视频无码国产 | 欧美三级午夜理伦三级中视频 | 黄色av网站在线观看 | 丰满熟女一级毛片视频 | 夜精品无码A片一区二区蜜桃 | 精品一区二区三区呻吟声 | 海角91成人一区二区三区 | 国产A∨无码片毛片一久 | 99久久无码一区人妻A片贼王 | 蜜桃狠狠色伊人亚洲综合 | 男女又爽 又黄 免费怀孕在线看 | 国产精品jizz中国一级片 | 人妻在厨房被强乱到舒服 | 亚洲高清在线观看视频 | 成人欧美精品久久久久影院 | 久久久久国色AV免费观看麻豆 | 国产精品三区在线观看 | 99久久久无码国产精品免费四季 | 人妻纶乱A级毛片免费看初女 | 国产18禁美女裸体爆乳无遮挡 | 日本一本二本在线观看 | 波多野结衣一区二区香蕉加勒比 |